谢孝军,杨亚丽,刘 俊,徐 德,张 海

目的：探究子宫体血管周上皮样细胞肿瘤（Perivascular Epithelioid Cell tumor，PEComa）的临床表现、病理及免疫表型特点、诊断与鉴别诊断。方法：选取本院2023年收治的1例术后病理诊断为子宫体血管周上皮样细胞肿瘤患者作为研究对象，并对其组织学形态观察和免疫组化染色检测进行分析，并进行相关文献复习，为女性生殖系统血管周上皮样细胞肿瘤做进好资料积累。结果：患者子宫血管周上皮样细胞肿瘤（PEComa）发生于子宫左前侧肌壁；细胞圆到卵圆、形态较一致，胞质空亮，核分裂象罕见。免疫组化提示HMB45(+),Melan-A(个别+)，SMA（－）S-100(-)。结论：子宫体血管周上皮样细胞肿瘤（PEComa）一种少见的间叶性肿瘤，其生物学性质仍未能明确，病理诊断较为困难，以组织形态学和免疫组织化学结合为主的方式有助于正确鉴别诊断。

子宫体肿瘤；PEComa；病理特征；鉴别诊断

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