郑丽君,胡宏鸯

无痛无汗症是一种在患者婴幼儿时期即可发病的遗传性感觉和自主神经病，其典型临床特征包括疼痛感知障碍、无汗和智力障碍，易发生高热、自残行为和各种意外损伤。既往研究显示CIPA患者死亡率高，生存期短，且目前尚无根治方法，只能通过积极预防并发症和对症支持治疗来减轻疾病影响。因此，本研究综述了CIPA患者并发症管理策略，旨在为该罕见病患者的医疗照护和健康教育提供借鉴。

无痛无汗症；遗传性感觉和自主神经病；并发症；自残行为；综述

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